RESUMO
Background: From the first description in 1886, significant progress was made on the treatment of Ebstein disease by mono and bi-ventricular surgery
Aim: To highlight the prognosis of Ebstein's anomaly in the pediatric department of Hassan II hospital in Fez
Methods: This is a descriptive and retrospective study of 4 years
Results: We collected nine patients [seven boys and two girls] with a mean age of 5.3 years. Cyanosis was the main mode of revelation of the disease. In three patients Ebstein's anomaly was part of a malformative syndrome. All patients had only symptomatic medical treatment. Five patients are still alive at a follow up of one to six years
Conclusion: Symptomatic medical treatment of Ebstein malformation may improve the prognosis of the disease